Volume 9, Issue 4 (10-2021)                   J. Pediatr. Rev 2021, 9(4): 321-328 | Back to browse issues page

XML Print

Download citation:
BibTeX | RIS | EndNote | Medlars | ProCite | Reference Manager | RefWorks
Send citation to:

Jafari N, Jafari R. Orbital Lymphangioma: A Case Report and Review of Management Modalities. J. Pediatr. Rev 2021; 9 (4) :321-328
URL: http://jpr.mazums.ac.ir/article-1-362-en.html
1- Student Research Committee, Faculty of Medicine, Mazandaran University of Medical Sciences, Sari, Iran.
2- Department of Ophthalmology, Faculty of Medicine, Mazandaran University of Medical Sciences, Sari, Iran. , rezaj76@yahoo.com
Abstract:   (1411 Views)
Background: Generally presents in childhood, orbital lymphangioma is an uncommon unencapsulated vascular malformation of the lymphatic system. These benign cystic lesions represent 1%-4% of all orbital masses and may appear after an upper respiratory infection or minor trauma. Because of its nature, the management can be challenging and depends on the clinical presentation. We report an 8-year-old boy with orbital lymphangioma presented with acute proptosis. Then, we discuss different features of this disorder plus its management 
Case Presentation: An 8-year-old boy was presented with sudden left eye proptosis. He had normal visual acuity and color vision without ocular pain or diplopia. An infiltrative and diffused intraconal plus extraconal mass was detected in orbital computed tomography. Contrast-enhanced MRI revealed a multilobulated infiltrative heterogeneous lesion with fluid-fluid levels. The diagnosis was made on imaging, and he went under treatment with an oral corticosteroid. The symptoms were entirely resolved, and no recurrence occurred during the follow-up. There are several surgical and nonsurgical therapies for orbital lymphangioma. Still, the priority is conservative management, such as sclerotherapy (including OK-432, doxycycline, sodium tetradecyl sulfate, etc.), bleomycin, carbon dioxide laser, systemic corticosteroids, and so on.
Conclusions: In most cases, the current imaging methods make a noninvasive diagnosis of orbital lymphangioma possible. Conservative management should be considered the first treatment.
Full-Text [PDF 927 kb]   (947 Downloads) |   |   Full-Text (HTML)  (386 Views)  
Type of Study: Case Report and Review of Literature | Subject: Ophthalmology
Received: 2020/09/27 | Accepted: 2021/05/9 | Published: 2021/10/1

Add your comments about this article : Your username or Email:

Send email to the article author

Rights and permissions
Creative Commons License This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.

© 2023 CC BY-NC 4.0 | Journal of Pediatrics Review

Designed & Developed by : Yektaweb