Volume 9, Issue 4 (In Press 2021)                   J. Pediatr. Rev 2021, 9(4): 6-6 | Back to browse issues page

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Jafari N, Jafari R. Orbital Lymphangioma: A Case Report and Review of Management Modalities. J. Pediatr. Rev. 2021; 9 (4) :6-6
URL: http://jpr.mazums.ac.ir/article-1-362-en.html
1- Faculty of Medicine, Student Research Committee, Mazandaran University of Medical Sciences, Sari, Iran.
2- Department of Ophthalmology, Faculty of Medicine, Mazandaran University of Medical Sciences, Sari, Iran. , rezaj76@yahoo.com
Abstract:   (563 Views)
Introduction: Orbital lymphangioma which generally presents in childhood is an uncommon unencapsulated vascular malformation of the lymphatic system. These benign cyst lesions represent 1-4% of all orbital masses and may appear after an upper respiratory infection or minor trauma. Because of its nature management can be challenging and depends on the clinical presentation. We describe a case of an 8-year-old boy with orbital lymphangioma which presented as acute proptosis and discuss about different features and management of this malformation.
Case presentation: The case was an 8-year-old boy with sudden left eye proptosis. He had normal visual acuity and color vision without ocular pain or diplopia. An infiltrative and diffused intraconal and extraconal mass was shown in Orbital computed tomography. Contrast-enhanced MRI revealed a multilobulated infiltrative heterogeneous lesion with fluid-fluid levels. Diagnosis was made on imaging and he went under treatment with corticosteroid. The symptoms were completely resolved and no recurrence occurred during the follow up period. There are several surgical and non-surgical managements for orbital lymphangioma but conservative management such as sclerotherapy (including ok-432, doxycycline, sodium tetradecyl sulfate etc.), bleomycin, carbon dioxide laser, systemic corticosteroids etc. is the first priority.
Conclusion: In most cases, Current methods make non-invasive diagnosis of orbital lymphangioma possible and conservative management should be considered as the first-line treatment.
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Type of Study: Case Report and Review of Literature | Subject: Ophthalmology
Received: 2020/09/27 | Accepted: 2021/05/9 | Published: 2021/10/23

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